Proceedings of 2015 Innovations in Pediatric Heart Failure Symposium
Heart failure in children is a rare disease that often leads to poor clinical outcomes. For example, the incidence of dilated cardiomyopathy in childhood is relatively small as compared to other childhood diseases, estimated at 0.57 cases per 100,000 per year in the US. However, nearly half of these children (46%) will die or require heart transplantation within five years of presentation [1]. With the improvement in outcomes for children with congenital heart disease, the management of heart failure in survivors of congenital heart surgery has become a significant burden for many pediatric and adult congenital cardiac cen...
Source: Progress in Pediatric Cardiology - November 30, 2016 Category: Cardiology Authors: Rakesh K. Singh, Anthony C. Chang, Jeffrey A. Towbin, Steven E. Lipshultz Tags: Preface Source Type: research
Editorial Board
(Source: Progress in Pediatric Cardiology)
Source: Progress in Pediatric Cardiology - November 30, 2016 Category: Cardiology Source Type: research
Risk of stroke in patients with right-sided congenital heart disease and interatrial communication
The association between patent oval foramen and cryptogenic stroke has been well described. The reported rate of stroke in young adults is between 6 and 11 per 100,000 patient-years and between 50 and 147 per 100,000 patient-years in adults with congenital heart disease. The purpose of this study was to evaluate the rate of stroke in a subset of patients with congenital heart disease: in patients with right-sided congenital heart disease and interatrial communication. This is a retrospective review of the clinical data from the McGill Adult Unit for Congenital Heart Disease and the Jewish General Hospital Congenital Clinic...
Source: Progress in Pediatric Cardiology - November 22, 2016 Category: Cardiology Authors: Claudia Renaud, Malak El Rayes, Maria Victoria Ordonez, Ariane Marelli, Judith Therrien Source Type: research
Double heterozygous mutation positive familial hypertrophic cardiomyopathy associated with early-onset sudden cardiac arrest
We report a case of a child with known double-heterozygous mutations causative of HCM. The child had evidence of HCM by 4months of age, and experienced aborted cardiac death starting at 7years of age. (Source: Progress in Pediatric Cardiology)
Source: Progress in Pediatric Cardiology - November 17, 2016 Category: Cardiology Authors: Kaitlyn Freeman, Frank Cecchin, Anna Tsirka Source Type: research
Improving communication with families of patients undergoing pediatric cardiac surgery
Peri-operative communication between families and parents of children undergoing pediatric cardiac surgery remains uneven and is felt to contribute to variation in subjective perceptions and inclusion by parents. We conducted a series of structured interviews and surveys in a prospective mixed-method study at a 140 bed university-affiliated tertiary pediatric hospital with approximately 6300 annual admissions. All English speaking patients undergoing pediatric cardiac surgery were eligible for inclusion. (Source: Progress in Pediatric Cardiology)
Source: Progress in Pediatric Cardiology - November 16, 2016 Category: Cardiology Authors: Christina Lopez, Cherissa C Hanson, Diane Yorke, Julie K Johnson, Michael R Mill, Karla J Brown, Paul Barach Source Type: research
Developing a subspecialty fellow education program: Covering topics common to all pediatric subspecialties
There is great value in developing a Fellowship Research and Education Seminar Series that targets all subspecialty fellows in a Pediatric Department. There are many topics that are common to all subspecialties that can be covered in this forum and obviate the need for each division to have these as separate educational activities. This can be a particularly useful supplement to divisions that may not have faculty with expertise in the wide variety of topics related to research and teaching that are covered. (Source: Progress in Pediatric Cardiology)
Source: Progress in Pediatric Cardiology - November 16, 2016 Category: Cardiology Authors: Robert D. Ross, Deepak Kamat Tags: Discussion Source Type: research
Congenital Giant aneurysm of the right atrial appendage: Fetal diagnosis and treatment
Giant aneurysm of the right atrial appendage is an exceedingly rare congenital abnormality. Only eight previous cases of right atrial appendage aneurysm (RAAA) present in neonates could be identified in the literature to date. The etiology and natural history of this condition remains poorly understood. Here we present the case of a giant RAAA diagnosed in utero at 20weeks gestation and which enlarged steadily until birth. The condition was corrected surgically by aneurysmectomy at three weeks of age. (Source: Progress in Pediatric Cardiology)
Source: Progress in Pediatric Cardiology - October 30, 2016 Category: Cardiology Authors: Alexander N. Goel, Andrew C. Fiore Source Type: research
Intraindividual validation of ventricular volume measurement by aortic and pulmonary arterial flow measurements in routine clinical cardiovascular magnetic resonance of congenital heart disease
To validate right and left ventricular stroke volume (RVSV& LVSV) measurements by forward flow stroke volume from aortic (AoSV) and pulmonary arterial (MPASV) measurements during routine cardiovascular magnetic resonance (CMR) in congenital heart disease (CHD). (Source: Progress in Pediatric Cardiology)
Source: Progress in Pediatric Cardiology - October 28, 2016 Category: Cardiology Authors: Ahmed Kharabish, Fransis Ghandour, Naira Mkrtchyan, Christian Meierhofer, Stefan Martinoff, Peter Ewert, Heiko Stern, Sohrab Fratz Source Type: research
Prenatal diagnosis of juxtaposition of the right atrial appendage before the third trimester of pregnancy. Importance of the 4 chamber plane
In 1893 Birmingham [1] first described a specimen with two atrial appendages side-by-side to the left of the great arteries. In 1954, Dixon [2] reported the first case with both atrial appendages to the right of the great arteries and suggested the term “juxtaposition of the atrial appendages” (JAA). This is a rare congenital heart malformation where the appendages are morphologically normal but arise ectopically from the anterior wall of the corresponding atrium, so both are located to the right (right juxtaposition) or to the left (left juxta position) of the great arteries. (Source: Progress in Pediatric Cardiology)
Source: Progress in Pediatric Cardiology - October 5, 2016 Category: Cardiology Authors: Carolina Blanco Rodr íguez, Victor Bautista Hernández, Fernando Rueda Nuñez Source Type: research
The potential of novel peptides in the management of children with Congenital Heart Disease: Above and beyond the BNP
Congenital Heart Disease (CHD) constitutes a common cause of major congenital abnormalities with prevalence around 8.2 per 1000 live births in Europe. Despite the important advances in the diagnosis, treatment and management of CHD patients throughout the years, it remains a challenge how to better manage the children with CHD using the biomarkers. However, in the last decade, B-type Natriuretic Peptide (BNP) and less often Adrenomedullin (ADM) and Urotensin II (UT II) have become the focus of research, in view of the improvement in the management of patients with CHD. (Source: Progress in Pediatric Cardiology)
Source: Progress in Pediatric Cardiology - October 4, 2016 Category: Cardiology Authors: Papachristou Panagiota, Varounis Christos, Grigoriadou Georgia, Garoufi Anastasia Tags: Review Source Type: research
Prevalence of ideal cardiovascular health metrics in children & adolescents: A systematic review
Although the prevalence of ideal cardiovascular health (CVH) has been extensively studied, its distribution in younger populations is not well established. In this systematic review we aggregated available evidence to examine prevalence of ideal CVH metrics in the adolescent and children population. (Source: Progress in Pediatric Cardiology)
Source: Progress in Pediatric Cardiology - September 12, 2016 Category: Cardiology Authors: Justin M. Pacor, Adnan Younus, Rehan Malik, Chukwuemeka U. Osondu, Muhammad Aziz, Oluseye Ogunmoroti, Muhammad Amir Younus, Ehimen C. Aneni, Erica S. Spatz, Choudhry Humayun, Salim Virani, Michael Blaha, Khurram Nasir Tags: Review Source Type: research
Assessment of the longevity of valves placed in the pulmonary position in patients with congenital heart disease
Pulmonary valve replacement is often performed in patients with complex congenital heart disease with pathology involving the right ventricular outflow tract. Progressive valve dysfunction is a well-described phenomenon. The aim of this study was to compare the longevity of homograft and bioprosthetic valves placed in the pulmonary position and to determine factors influencing valve dysfunction. We conducted a retrospective chart review of all patients who underwent surgical pulmonary valve replacement with homograft or bioprosthetic (bovine pericardial or porcine) valves during the period January 2000 through December 201...
Source: Progress in Pediatric Cardiology - September 12, 2016 Category: Cardiology Authors: Juanita Hunter, Eliot Rosenkranz, Hua Li, Sethuraman Swaminathan Source Type: research
The United States Pediatric Cardiology 2015 Workforce Assessment: A survey of current training and employment patterns
The number of pediatric cardiology trainees in the United States doubled between 2004 and 2015, but there is a lack of information on the current pediatric cardiology workforce. Therefore, a survey was administered to members of the American Academy of Pediatrics Section on Cardiology and Cardiac Surgery and to non-duplicative board-certified or board-eligible pediatric cardiologists. Of 2897 individuals contacted, 823 completed the survey (28%), with a higher response rate among program directors (87%) and division chiefs (71%). (Source: Progress in Pediatric Cardiology)
Source: Progress in Pediatric Cardiology - September 8, 2016 Category: Cardiology Authors: Robert D. Ross, Shubhika Srivastava, Antonio G. Cabrera, Holly S. Ruch-Ross, Carrie L. Radabaugh, L. LuAnn Minich, William T. Mahle, David W. Brown Source Type: research
Introduction by Guest Editor:
The challenges facing pediatric heart programs present an opportunity to re-envision the traditional leadership structure and create a novel paradigm that focuses on culture, citizenship and leadership at every level. It is imperative that we begin to “think disruptively” not only about how we advance innovations in patient care, but also how we disseminate our collaborative philosophy across our multi-disciplinary teams. The following articles depict the foundations for creating a program with successful culture, citizenship and leadership. (Source: Progress in Pediatric Cardiology)
Source: Progress in Pediatric Cardiology - August 31, 2016 Category: Cardiology Authors: John R. Charpie, Stefanie L. Peters Source Type: research
Dyad Leadership: 1+1= > 2
Background (Source: Progress in Pediatric Cardiology)
Source: Progress in Pediatric Cardiology - August 31, 2016 Category: Cardiology Authors: Susan Collins, Jeffrey Jacobs, Richard Perryman Source Type: research
