Implantable cardioverter defibrillators and biventricular pacing in pediatric dilated cardiomyopathy: Preventing death and delaying heart transplant
Dilated cardiomyopathy (DCM) is a frequent cause of mortality and heart transplantation in pediatric patients. Device therapy has been shown to improve mortality and transplantation rates in adult patients with dilated cardiomyopathy. However, the criteria that are used to guide implantable cardioverter defibrillators (ICDs) and cardiac resynchronization therapy (CRT) devices in adult patients cannot be directly applied to pediatric patients. ICDs are a proven treatment for the prevention of sudden cardiac death (SCD), but it is difficult to quantify SCD in the pediatric DCM population. (Source: Progress in Pediatric Cardiology)
Source: Progress in Pediatric Cardiology - April 16, 2018 Category: Cardiology Authors: Rohan Kumthekar, Charles I. Berul Tags: Review Source Type: research
Cardiac rehabilitation in pediatric cardiomyopathy
Pediatric cardiomyopathies affect a small portion of the pediatric population, but the constellation of disorders encompasses a wide range of symptoms and disease severity. Medical and surgical therapies have continued to advance, and combined with increasing data from adult studies, cardiac rehabilitation likely has an important role in the care of these children as data shows benefits ranging from improved endothelial function to improved quality of life. While there are limited guidelines for exercise training and sports participation in children with cardiomyopathy, data to shape these guidelines remains sparse and the...
Source: Progress in Pediatric Cardiology - April 11, 2018 Category: Cardiology Authors: Philip T. Thrush, Casey Vogel Tags: Review Source Type: research
An atypical right ventricle-dependent coronary circulation in a child with pulmonary artery stenosis
We report the first case of RVDCC in a child with main pulmonary artery stenosis and normal RV development. (Source: Progress in Pediatric Cardiology)
Source: Progress in Pediatric Cardiology - April 5, 2018 Category: Cardiology Authors: Nabil Tahhan, Lucile Houyel, Jerome Petit, Jurgen Horer, Sebastien Hascoet Source Type: research
Stenting of the right ventricular outflow tract after late thrombosis of a modified Blalock-Taussig shunt in an infant with tetralogy of Fallot and right pulmonary artery agenesis
We present the case of right ventricular outflow tract stenting in an 8-month girl with tetralogy of Fallot and right pulmonary artery agenesis after late thrombosis of the left-sided modified Blalock-Taussig shunt. (Source: Progress in Pediatric Cardiology)
Source: Progress in Pediatric Cardiology - March 26, 2018 Category: Cardiology Authors: Ilya Soynov, Yuriy Kulyabin, Artem Gorbatykh, Alexey Zubritskiy, Igor Kornilov, Nataliya Nichay, Alexander Omelchenko, Alexey Voitov Source Type: research
Risk stratification in pediatric hypertrophic cardiomyopathy: Insights for bridging the evidence gap?
Identification of children with hypertrophic cardiomyopathy (HCM) who are at high risk for sudden cardiac death (SCD) remains challenging. Although a large number of risk factors have been implicated in HCM associated SCD, evidence for individual risk factors are not robust. Current risk prediction models are extrapolated from adult HCM and have low positive predictive value when applied to the pediatric HCM population. Clinical factors that are strongly associated with SCD in children with HCM are limited to previous adverse cardiac event, prior syncope and extreme left ventricular hypertrophy; there are variable conclusi...
Source: Progress in Pediatric Cardiology - March 22, 2018 Category: Cardiology Authors: Stephanie J. Nakano, Shaji C. Menon Tags: Review Source Type: research
Utilization of VADs in children with restrictive and hypertrophic cardiomyopathy: Are we there yet?
Pediatric Ventricular assist device (VAD) use in pediatrics has increased dramatically over the last decade. Over a quarter of children are currently supported with a VAD until a suitable organ becomes available. The majority of these patients have dilated cardiomyopathy (DCM), though some have congenital heart disease, restrictive cardiomyopathy (RCM) or hypertrophic cardiomyopathy (HCM). Patients with restrictive cardiomyopathy or hypertrophic cardiomyopathy remain difficult to support due to anatomic limitations and the limited number of devices currently available to children. (Source: Progress in Pediatric Cardiology)
Source: Progress in Pediatric Cardiology - March 20, 2018 Category: Cardiology Authors: Chet Villa, John Broderick, Raheel Rizwan, Angela Lorts Tags: Review Source Type: research
A child with acquired Gerbode defect due to infective endocarditis: Successful percutaneous closure with Nit-occlud device ®
We report a rare case of a child with an acquired Gerbode defect following Infective Endocarditis of the tricuspid valve which was successfully closed with a Nit-Occlud device®. There are only a few reports of Gerbode defect percutaneously closed using this d evice, especially in the young pediatric population. (Source: Progress in Pediatric Cardiology)
Source: Progress in Pediatric Cardiology - March 20, 2018 Category: Cardiology Authors: P. Éden Santos, N.G. Villanueva, F. Ballesteros, M.A. Matamala-Morillo, J.L. Zunzunegui Source Type: research
Utilization of VADs in children with restrictive and hypertrophic cardiomyopathy: Are we there yet?
Pediatric Ventricular assist device (VAD) use in pediatrics has increased dramatically over the last decade. Over a quarter of children are currently supported with a VAD until a suitable organ becomes available. The majority of these patients have dilated cardiomyopathy (DCM), though some have congenital heart disease, restrictive cardiomyopathy (RCM) or hypertrophic cardiomyopathy (HCM). Patients with restrictive cardiomyopathy or hypertrophic cardiomyopathy remain difficult to support due to anatomic limitations and the limited number of devices currently available to children. (Source: Progress in Pediatric Cardiology)
Source: Progress in Pediatric Cardiology - March 20, 2018 Category: Cardiology Authors: Chet Villa, John Broderick, Raheel Rizwan, Angela Lorts Tags: Review Source Type: research
A child with acquired Gerbode defect due to infective endocarditis: Successful percutaneous closure with Nit-occlud device ®
We report a rare case of a child with an acquired Gerbode defect following Infective Endocarditis of the tricuspid valve which was successfully closed with a Nit-Occlud device®. There are only a few reports of Gerbode defect percutaneously closed using this d evice, especially in the young pediatric population. (Source: Progress in Pediatric Cardiology)
Source: Progress in Pediatric Cardiology - March 20, 2018 Category: Cardiology Authors: P. Éden Santos, N.G. Villanueva, F. Ballesteros, M.A. Matamala-Morillo, J.L. Zunzunegui Source Type: research
