Ostre uszkodzenie nerek u ch łopca z urosepsą o etiologii Pseudomonas aeruginosa po zabiegu resekcji zastawek cewki tylnej
We present case of a 21-month-old boy with AKI due to Pseudomonas aeruginosa urosepsis after posterior urethral valves (PUV) resection. Implementation of appropriate treatment including intensive antibiotic therapy with dosage adjustment to renal function, gentamicin concentration monitoring, appropriate fluid therapy and bladder catheterization to allow the outflow of urine, resulted in full recovery from urosepsis and normalization of serum creatinine concentration. Because of the urinary tract defect, the episode of AKI, and presence of microalbuminuria after 3 months of observation, prognosis for the development of chr...
Source: Pediatria Polska - August 24, 2016 Category: Pediatrics Source Type: research

Gastric outlet obstruction caused by duplication of duodenum – A case report and review of literature
Publication date: Available online 23 August 2016 Source:Pediatria Polska Author(s): Ewa Matuszczak, Wojciech Debek, Katarzyna Kondej-Muszynska, Monika Kowalczuk, Dariusz Lebensztejn, Adam Hermanowicz Gastrointestinal tract duplications are rare congenital lesions. They can occur anywhere from the mouth to the anus with a reported incidence of 1 in 18.00 to 1 in 4500 live births. Duodenal duplication cysts represent 2–12% of all duplications. Authors present the case of 5-month-old boy admitted to Pediatric Surgery Department with the symptoms of mechanical obstruction of alimentary tract and gastrointestinal ble...
Source: Pediatria Polska - August 23, 2016 Category: Pediatrics Source Type: research

Adiponektyna – hormon regulujący rozwój dziecka: aktualny stan wiedzy
Publication date: Available online 21 August 2016 Source:Pediatria Polska Author(s): Dominika Wiśniewska-Ulfik, Urszula Godula-Stuglik, Magdalena Wąsek-Buko Adiponectin is a cytokine built with 244 amino acids. It is produced and secreted by adipose tissue. The concentration of this hormone in serum fluctuates from 1 to 30μg/ml. The main function of this cytokine is the control of metabolism, carbohydrates and lipids. Women have higher concentration of adiponectin than men. Its high concentration is observed in those suffering from anorexia and bulimia. Its reduced concentration decreases insulin levels, and leads ...
Source: Pediatria Polska - August 20, 2016 Category: Pediatrics Source Type: research

Clinical effectiveness of amino acid formula in infants with severe atopic dermatitis and cow's-milk protein allergy
Conclusions: The described positive treatment effects were obtained with the diet duration of 4 weeks, the optimal period for the elemental diet administration needs further investigation. (Source: Pediatria Polska)
Source: Pediatria Polska - August 20, 2016 Category: Pediatrics Source Type: research

Obustronna implantacja ślimakowa – korzyści i trudności
Publication date: Available online 20 August 2016 Source:Pediatria Polska Author(s): Katarzyna Ita Bieńkowska The introduction of cochlear implants has changed daily life of people with profound hearing impairment as it allows auditive contact with the environment and gives them a possibility of mastering verbal speech, increasing their sense of security and giving them more leisure time possibilities. It has been more than 20 years since the first cochlear implant surgery took place in Poland. Initially, patients were satisfied with unilateral hearing. With time, the monitoring techniques have been improved and there ...
Source: Pediatria Polska - August 19, 2016 Category: Pediatrics Source Type: research

An extensive Fibrous dysplasia of anterior skull base area of a 12-year-old boy – A case report
We report a rare case of fibrous dysplasia involving extensively anterior skull base in a pediatric patient without presenting any clinical manifestation except swelling in right side facial area. As patient is asymptomatic, he is carefully monitored by us to treat earliest if symptoms appear. (Source: Pediatria Polska)
Source: Pediatria Polska - August 19, 2016 Category: Pediatrics Source Type: research

The investigation of the causes of failure to thrive among children referred to health centers based on the health belief model
Conclusion The results of this study showed that there is a significant association between social factors and failure to thrive. The findings also indicated that household size, income, mothers’ knowledge, perceived severity, and perceived benefits are associated with failure to thrive. Therefore, educational intervention for family planning is recommended for nutrition patterns in order to regulate household size and promote mothers’ knowledge and self-efficiency. (Source: Pediatria Polska)
Source: Pediatria Polska - August 19, 2016 Category: Pediatrics Source Type: research

Neurogenic bladder as a symptom of caudal regression syndrome
We report 2 children with CRS associated with neurogenic bladder. In the first patient, CRS was revealed during evaluation of recurrent urinary tract infections (UTIs). In the second one, CRS led to chronic kidney disease (CKD) as a result of patient's poor compliance. (Source: Pediatria Polska)
Source: Pediatria Polska - August 17, 2016 Category: Pediatrics Source Type: research

Ivar Asbj ørn Følling – człowiek, który odkrył fenyloketonurię
Publication date: Available online 26 July 2016 Source:Pediatria Polska Author(s): Dariusz Walkowiak The present paper focuses on the person of distinguished scientist, the discoverer of phenylketonuria, Ivar Asbjørn Fölling. His life was presented, from his childhood on a provincial farm to the main research conducted by Fölling and finally the awards and orders received. The researcher was positioned in the wider context of changes taking place in Norway after the recovery of the country's full sovereignty in 1905. Besides the most important achievement, which was undoubtedly the discovery of phenylketonuria in 193...
Source: Pediatria Polska - August 8, 2016 Category: Pediatrics Source Type: research

Ostre zapalenie trzustki w przebiegu leczenia padaczki kwasem walproinowym u dwojga dzieci
Publication date: Available online 6 August 2016 Source:Pediatria Polska Author(s): Agnieszka Borys-Iwanicka, Tatiana Jamer, Barbara Iwańczak Valproic acid, frequently used in the treatment of epilepsy, may be one of the causes of acute pancreatitis in children. In our work we have described acute pancreatitis in a 5-year-old girl and a 16-year-old boy who were treated with valproic acid. The girl, with infant cerebral palsy, hydrocephalus, retarded development and epilepsy had been treated with valproic acid for four years. The boy had been treated with valproic acid for three months due to numbness episodes and uns...
Source: Pediatria Polska - August 6, 2016 Category: Pediatrics Source Type: research

Historia Oddzia łu Kardiologii Dziecięcej Śląskiego Centrum Chorób Serca w Zabrzu 1986–2016
Publication date: Available online 6 August 2016 Source:Pediatria Polska Author(s): Sylwia Sulik-Gajda Pediatric Cardiology is a young, rapidly growing field of medicine. The beginning of this discipline in world dates back to 40s of the twentieth century, when the first doctors training started in the field of heart disease in children. In Silesia, the first attempts to develop this branch of medicine were taken in the 80s of the twentieth century. The Department of Pediatric Cardiology in Zabrze is one of the resulting centers for diagnosis and treatment of children with heart disease, and it was founded by Dr. Lili G...
Source: Pediatria Polska - August 6, 2016 Category: Pediatrics Source Type: research

Errata do artyku łu: Prof. Irena Obuchowska (1931–2016) – psycholog z wykształcenia, pedagog z powołania, wielki przyjaciel dzieci [Pediatria Polska 2016;91(4): 395–397]
Publication date: Available online 3 August 2016 Source:Pediatria Polska Author(s): Marian Krawczyński (Source: Pediatria Polska)
Source: Pediatria Polska - August 3, 2016 Category: Pediatrics Source Type: research

Pierwotna niedoczynno ść nadnerczy u dzieci
Publication date: Available online 28 July 2016 Source:Pediatria Polska Author(s): Elżbieta Lipska, Ewelina Witkowska-Sędek, Beata Pyrżak Primary adrenal insufficiency (PAI) consists one of the most critical life-threatening conditions in paediatric endocrinology. Authors present PAI pathophysiology and current Endocrine Society Clinical Practice Guideline for diagnosis and treatment in children. (Source: Pediatria Polska)
Source: Pediatria Polska - July 28, 2016 Category: Pediatrics Source Type: research

Obj ęcie młodzieży leczonej w dzieciństwie z powodu nowotworu opieką medyczną dla dorosłych
Publication date: Available online 25 July 2016 Source:Pediatria Polska Author(s): Maryna Krawczuk-Rybak Systematic improvement of treatment of neoplastic diseases in childhood resulted in a growing population of survivors which are threatened by a number of late effects of therapy. The possibility of organ damage, which can occur even after several years off the therapy, is known to paediatric oncologists, but not always to other specialists and primary care physicians, and neither to the patients. A major problem is the transition of young cancer survivors from paediatric to adult multidisciplinary care. Adolescent...
Source: Pediatria Polska - July 25, 2016 Category: Pediatrics Source Type: research

Badania IQ u chorych na fenyloketonuri ę w latach siedemdziesiątych i osiemdziesiątych XX wieku
Publication date: Available online 1 July 2016 Source:Pediatria Polska Author(s): Dariusz Walkowiak, Łukasz Kałużny, Anna Bukowska-Posadzy Phenylketonuria (PKU) is currently regarded as a model example of an inborn error of metabolism. An important parameter of the assessment of patients is analysis of intellectual functioning. The present article is the continuation of the work whose first part was concerned with the 1950s and 1960s. It deals with the development of research in the 1970s and 1980s. It was a period when, due to the doubts regarding the quality of the research on the effectiveness of diet, mult...
Source: Pediatria Polska - July 22, 2016 Category: Pediatrics Source Type: research