Physical exercise training for cystic fibrosis
(Source: Paediatric Respiratory Reviews)
Source: Paediatric Respiratory Reviews - January 2, 2016 Category: Respiratory Medicine Authors: Thomas Radtke, Sarah J Nolan, Helge Hebestreit, Susi Kriemler Source Type: research
Physical exercise training for cystic fibrosis
Cystic fibrosis (CF) is the most common life-shortening autosomal recessively inherited disease in Caucasian populations [2]. Progressive respiratory disease in CF results in an abnormal ventilatory response to exercise which contributes to dyspnea and is a major limiting factor to exercise tolerance [3]. In addition, a sedentary lifestyle contributes to the progression of physical and functional impairment in CF [4], likely with the consequence of a reduced life expectancy as exercise capacity is linked to survival [5]. (Source: Paediatric Respiratory Reviews)
Source: Paediatric Respiratory Reviews - January 1, 2016 Category: Respiratory Medicine Authors: Thomas Radtke, Sarah J. Nolan, Helge Hebestreit, Susi Kriemler Tags: Cochrane Corner Source Type: research
Primary Ciliary Dyskinesia
The diagnosis of Primary Ciliary Dyskinesia [PCD] is often delayed or missed [1]. Whilst there is some evidence for the age of diagnosis falling by two years to an age of 5 years over the last 15 years [2], many clinicians struggle to consider the diagnosis of PCD in young children when the presenting symptoms will overlap with common transient respiratory infections. The key considerations include the recurrent nature of the airway infections, persisting symptoms and associated features, particularly in children with heterotaxy and situs abnormalities [3]. (Source: Paediatric Respiratory Reviews)
Source: Paediatric Respiratory Reviews - December 29, 2015 Category: Respiratory Medicine Authors: Dominic A. Fitzgerald, Adam J. Shapiro Tags: Mini-symposium Source Type: research
Mini-symposium Primary Ciliary Dyskinesia
(Source: Paediatric Respiratory Reviews)
Source: Paediatric Respiratory Reviews - December 29, 2015 Category: Respiratory Medicine Authors: Dominic A. Fitzgerald, Adam J. Shapiro Source Type: research
Inhaled Mannitol (Bronchitol) for Cystic Fibrosis
Cystic fibrosis (CF) is the most common autosomal recessive, life-limiting disorder in Caucasian populations, occurring in approximately 1 in 2500 live births [2]. In the USA and the UK, approximately 1 in 25 Caucasian people are carriers of a CFTR abnormality [3,4]. (Source: Paediatric Respiratory Reviews)
Source: Paediatric Respiratory Reviews - December 28, 2015 Category: Respiratory Medicine Authors: Sarah J. Nolan, Judith Thornton, Clare S. Murray, Tiffany Dwyer Tags: Cochrane Corner Source Type: research
Cochrane Corner - Inhaled Mannitol (Bronchitol) for Cystic Fibrosis
(Source: Paediatric Respiratory Reviews)
Source: Paediatric Respiratory Reviews - December 28, 2015 Category: Respiratory Medicine Authors: Sarah J Nolan, Judith Thornton, Clare S Murray, Tiffany Dwyer Source Type: research
The respiratory consequences of early-term birth and delivery by caesarean sections
In England and Wales, 19% of live births in 2012 were at 37-38 weeks’ gestation, equating to nearly 140 000 early-term births each year. Since caesarean sections (CS) are often performed at early-term gestations, this accounts for some of the increased proportion of the early-term births. Infants born early-term are at an increased risk of neonatal respiratory morbidity particularly if they are delivered by caesarean section. The long term lung function data are limited but available data suggest that early-term delivery is associated with respiratory morbidity in childhood. (Source: Paediatric Respiratory Reviews)
Source: Paediatric Respiratory Reviews - December 22, 2015 Category: Respiratory Medicine Authors: Sarah J Kotecha, David J Gallacher, Sailesh Kotecha Source Type: research
The respiratory consequences of early-term birth and delivery by caesarean sections
In England and Wales, 19% of live births in 2012 were at 37-38 weeks ’ gestation, equating to nearly 140 000 early-term births each year. Since caesarean sections (CS) are often performed at early-term gestations, this accounts for some of the increased proportion of the early-term births. Infants born early-term are at an increased risk of neonatal respiratory mor bidity particularly if they are delivered by caesarean section. The long term lung function data are limited but available data suggest that early-term delivery is associated with respiratory morbidity in childhood. (Source: Paediatric Respiratory Reviews)
Source: Paediatric Respiratory Reviews - December 21, 2015 Category: Respiratory Medicine Authors: Sarah J. Kotecha, David J. Gallacher, Sailesh Kotecha Tags: Review Source Type: research
Whole Body Plethysmography: Practical Considerations
Pediatric pulmonary plethysmography is an important tool used in the diagnosis of lung diseases. Understanding the physiology underlying the functioning of the test can aid the health care provider in its interpretation. The following article reviews the basic science behind whole body plethysmography, and provides an overview of the types of plethysmographs available. Finally, the limitations of the available normative values are discussed. (Source: Paediatric Respiratory Reviews)
Source: Paediatric Respiratory Reviews - December 7, 2015 Category: Respiratory Medicine Authors: Zofia Zysman-Colman, Larry C. Lands Source Type: research
Motility, digestive and nutritional problems in Esophageal Atresia
Esophageal atresia (EA) with or without tracheoesophageal fistula (TEF) is a rare congenital malformation. Digestive and nutritional problems remain frequent in children with EA both in early infancy and at long-term follow-up. These patients are at major risk of presenting with gastroesophageal reflux and its complications, such as anastomotic strictures. Esophageal dysmotility is constant, and can have important consequences on feeding and nutritional status. Patients with EA need a systematic follow-up with a multidisciplinary team. (Source: Paediatric Respiratory Reviews)
Source: Paediatric Respiratory Reviews - December 4, 2015 Category: Respiratory Medicine Authors: Madeleine Gottrand, Laurent Michaud, Rony Sfeir, Frederic Gottrand Source Type: research
Oxygen and carbon dioxide monitoring during sleep
Monitoring of oxygen and carbon dioxide (CO2) is of crucial importance during sleep-disordered breathing in order to assess the consequences of respiratory events on gas exchange. Pulse oximetry (SpO2) is a simple and cheap method that is used routinely for the recording of oxygen levels and the diagnosis of hypoxemia. CO2 recording is necessary for the diagnosis of alveolar hypoventilation and can be performed by means of the end-tidal (PetCO2) or transcutaneous CO2 (PtcCO2). However, the monitoring of CO2 is not performed on a routine basis due to the lack of simple, cheap and reliable CO2 monitors. (Source: Paediatric Respiratory Reviews)
Source: Paediatric Respiratory Reviews - December 4, 2015 Category: Respiratory Medicine Authors: Alessandro Amaddeo, Brigitte Fauroux Source Type: research
Motility, digestive and nutritional problems in Esophageal Atresia
Esophageal atresia (EA) with or without tracheoesophageal fistula (TEF) is a rare congenital malformation. Digestive and nutritional problems remain frequent in children with EA both in early infancy and at long-term follow-up. These patients are at major risk of presenting with gastroesophageal reflux and its complications, such as anastomotic strictures. Esophageal dysmotility is constant, and can have important consequences on feeding and nutritional status. Patients with EA need a systematic follow-up with a multidisciplinary team. (Source: Paediatric Respiratory Reviews)
Source: Paediatric Respiratory Reviews - December 3, 2015 Category: Respiratory Medicine Authors: Madeleine Gottrand, Laurent Michaud, Rony Sfeir, Fr édéric Gottrand Tags: Mini-symposium: Esophageal Atresia and Tracheoesophageal Fistula Source Type: research
Oxygen and carbon dioxide monitoring during sleep
Monitoring of oxygen and carbon dioxide (CO2) is of crucial importance during sleep-disordered breathing in order to assess the consequences of respiratory events on gas exchange. Pulse oximetry (SpO2) is a simple and cheap method that is used routinely for the recording of oxygen levels and the diagnosis of hypoxemia. CO2 recording is necessary for the diagnosis of alveolar hypoventilation and can be performed by means of the end-tidal (PetCO2) or transcutaneous CO2 (PtcCO2). However, the monitoring of CO2 is not performed on a routine basis due to the lack of simple, cheap and reliable CO2 monitors. (Source: Paediatric Respiratory Reviews)
Source: Paediatric Respiratory Reviews - December 3, 2015 Category: Respiratory Medicine Authors: Alessandro Amaddeo, Brigitte Fauroux Tags: Clinical usefulness Source Type: research
