Generalized extensive cutaneous nodules as a first presentation of plasmablastic lymphoma in an immunocompetent patient: A case report and literature review
Publication date: Available online 28 September 2016 Source:Dermatologica Sinica Author(s): Eman Al Mussaed Plasmablastic lymphoma (PBL) is a rare aggressive non-Hodgkin lymphoma, frequently involving the jaw and oral mucosa in human immunodeficiency virus (HIV)-positive patients and is also often associated with Epstein–Barr virus infection, occurring mostly in men. However, a number of cases have been reported in extraoral sites and in immunocompetent patients. There have been no reported cases of PBL without immunodeficiency disease from Saudi Arabia presented by extensive cutaneous involvement. Here, we report a r...
Source: Dermatologica Sinica - October 1, 2016 Category: Dermatology Source Type: research
Multicentric reticulohistiocytosis in a Taiwanese woman with Sj ögren syndrome
Publication date: March 2016 Source:Dermatologica Sinica, Volume 34, Issue 1 Author(s): Lan-hsin Cheng, Ying-Yi Chiang Multicentric reticulohistiocytosis is a rare, non-Langerhans cell histiocytosis characterized by specific skin lesions and destructive arthritis. Clinically, it generally presents with multiple reddish-brown papulonodules over the hands, face, and trunk. The associated destructive arthropathy tends to be severe, with 50% of patients developing arthritis mutilans. Approximately 25–30% of patients present with neoplasia. Coexisting autoimmune diseases are also commonly reported. Here we report the ...
Source: Dermatologica Sinica - June 17, 2016 Category: Dermatology Source Type: research
Erythrodermic mycosis fungoides treated with low-dose methotrexate and 311 nm UV-B: A case report with 3-year follow up and literature review
Publication date: March 2016 Source:Dermatologica Sinica, Volume 34, Issue 1 Author(s): Yu-Hung Kuo, Chung-Hsing Chang Mycosis fungoides (MF) is a form of cutaneous T cell lymphoma defined by epidermotropism of a clonal T helper memory/effector subset. Erythrodermic MF usually presents a chronic course of MF with generalized erythema or poikiloderma but no systemic involvement, as in Sezary syndrome. Here we report a case of a 73-year-old Taiwanese male with a rapid progression of erythrodermic MF within 1.5 years. It was diagnosed after his fifth skin biopsy, which demonstrated a positive clonal band in the T cell...
Source: Dermatologica Sinica - June 17, 2016 Category: Dermatology Source Type: research
A novel nonsense mutation in CTSC causes Papillon –Lefèvre syndrome with uronephrosis
Publication date: June 2016 Source:Dermatologica Sinica, Volume 34, Issue 2 Author(s): Haiyan Song, Laicheng Wang, Li Zhang, Zhenying Wang (Source: Dermatologica Sinica)
Source: Dermatologica Sinica - June 17, 2016 Category: Dermatology Source Type: research
A novel mutation of the RNA-specific adenosine deaminase 1 gene in a Taiwanese patient with dyschromatosis symmetrica hereditaria and Becker's nevus-like lesion
Publication date: June 2016 Source:Dermatologica Sinica, Volume 34, Issue 2 Author(s): Yu-Chen Chen, Sheau-Chiou Chao, Mei-Hui Yang, Chao-Chun Yang (Source: Dermatologica Sinica)
Source: Dermatologica Sinica - June 17, 2016 Category: Dermatology Source Type: research
