Pierre Robin sequence with H-type tracheoesophageal fistula and congenital heart disease
Abstract: Pierre Robin sequence (PRs) is a congenital disease characterized by micrognathia, cleft palate, glossoptosis and a wide range of other anomalies. The treatment of patients with PRs may be problematic due to the varying anomalies and high mortality rate. In this case report, a 1-day-old newborn with micrognathia, cleft lip and palate, glossoptosis, a membranous ventricular septal defect and an H-type tracheoesophageal fistula has been evaluated and discussed considering the current literature. To the best of our knowledge, the coexistence of PRs with a membranous ventricular septal defect and H-type tracheoesopha...
Source: International Journal of Pediatric Otorhinolaryngology Extra - February 21, 2013 Category: ENT & OMF Authors: Nihat Demir, Erdal Peker, Oğuz Tuncer, Lokman Üstyol, Keziban Bulan Tags: Case reports Source Type: research

A rare case of necrotizing fasciitis of the external ear
Abstract: A 15 months old boy was referred to our emergency department with fever since 3 days and bilateral otorrhoe. Examination of the ears revealed an edematous and erythematous pinna at the left side, with necrosis of the tragus. Because of progression of the necrosis, an urgent debridement was performed and antimicrobial therapy was started.Necrotizing fasciitis (NF) is a progressive and potential fatal bacterial infection of the subcutaneous tissue, rapidly spreading along fascial planes. In the head and neck area NF is very uncommon. Most cases involve only the neck, usually from infections of dental or pharyngeal ...
Source: International Journal of Pediatric Otorhinolaryngology Extra - February 20, 2013 Category: ENT & OMF Authors: L. Van Crombrugge, H. Van Hoecke, N. Roche, I. Dhooge Tags: Case reports Source Type: research

Facial canal bifurcation with inner ear anomalies in a case of Klippel–Feil syndrome: A case report
We present a case of Klippel–Feil syndrome in a 2-year-old Chinese girl who presented with global developmental delay and bilateral profound hearing loss. High resolution computed tomography (HRCT) of temporal bones showed bilateral common cavity malformations with hypoplastic internal auditory canals and anomalous labyrinthine segments of both facial canals. The labyrinthine segment of the right facial canal was duplicated. Her brain magnetic resonance imaging (MRI) showed aplasia of both vestibulocochlear nerves, while the cisternal and intracanalicular segments of both facial nerves were of normal caliber. These conge...
Source: International Journal of Pediatric Otorhinolaryngology Extra - February 18, 2013 Category: ENT & OMF Authors: S.J.T. Tehrani, M.Z. Faizah, T.Y. Kew, A. Abdullah Tags: Case reports Source Type: research

Chondromyxoid fibroma of the nasal cavity in a pediatric patient: Case report and literature review
We report the case of a 5-year-old boy affected by a CMF of the ethmoid sinus invading the papyracea and ethmoidal roof. This is the second case of acquired CMF involving the sinonasal spaces in a pediatric patient. Although this neoplasm is very uncommon, particularly in young patients and at this anatomical site, it is very important to correctly diagnose these tumors for adequate treatment, which generally consists of surgical resection. (Source: International Journal of Pediatric Otorhinolaryngology Extra)
Source: International Journal of Pediatric Otorhinolaryngology Extra - February 15, 2013 Category: ENT & OMF Authors: Alberto Grammatica, Giulio Rossi, Davide Soloperto, Angelo Ghidini, Livio Presutti Tags: Case reports Source Type: research

Sinonasal solitary enchondroma: Case report and review of the literature
Abstract: Enchondromas are benign intramedullary tumors composed of nodules of hyaline cartilage. They are histologically distinct from chondromas, which are primarily soft tissue tumors. This is the first reported case in the literature of a solitary sinonasal enchondroma. Local recurrences are uncommon after gross total resection. More data are needed to conclude whether solitary sinonasal enchondromas can transform to malignant tumors, as has been reported with patients with multiple enchondromas such as in Maffucci's and Ollier's disease. (Source: International Journal of Pediatric Otorhinolaryngology Extra)
Source: International Journal of Pediatric Otorhinolaryngology Extra - February 11, 2013 Category: ENT & OMF Authors: Victor M. Duarte, Jeffrey D. Suh, Ali R. Sepahdari, Scott D. Nelson Tags: Case reports Source Type: research

Oral leiomyomatous hamartoma associated with upper lip midline malformation: Case report and review of the literature
Abstract: A 3-month-old male patient presented an upper lip malformation associated to a polypoid nodule in the maxillary anterior alveolar ridge. Microscopically, the nodule was predominantly composed by a non-encapsulated smooth muscle proliferation intermingled by numerous blood vessels of varied sizes and scattered small nerve fibers. The smooth muscle tissue was positive for desmin and smooth muscle actin, while endothelial cells were highlighted by CD34 staining. The final diagnosis was of an oral leiomyomatous hamartoma associated with upper lip malformation. After surgical treatment, no recurrence has been observed...
Source: International Journal of Pediatric Otorhinolaryngology Extra - January 14, 2013 Category: ENT & OMF Authors: Saulo Gabriel Moreira Falci, Ana Terezinha Marques Mesquita, Mário José Romañach, Oslei Paes de Almeida, Cássio Roberto Rocha dos Santos Tags: Case reports Source Type: research

List of Societies
(Source: International Journal of Pediatric Otorhinolaryngology Extra)
Source: International Journal of Pediatric Otorhinolaryngology Extra - January 1, 2013 Category: ENT & OMF Source Type: research

Luc's abscess—A case report
Abstract: Luc's abscess, a rare complication of otitis media, involves a subperiosteal collection beneath the temporalis muscle. This particular otitic abscess is not typically associated with mastoid infection and follows a rather benign course. As a result of its benign course, more conservative treatment may be attempted. However, with possible mastoid involvement, mastoidectomy may be required in addition to abscess drainage. (Source: International Journal of Pediatric Otorhinolaryngology Extra)
Source: International Journal of Pediatric Otorhinolaryngology Extra - December 26, 2012 Category: ENT & OMF Authors: Evan F. Garner, Brian J. McKinnon Tags: Case reports Source Type: research

Congenital laryngeal hamartoma with ectopic thymus causing airway compromise in a neonate
Abstract: To describe an interesting clinical and histopathologic case of a neonate presenting with respiratory distress and a laryngeal hamartoma with ectopic thymus and parathyroid tissue. Case report and PubMed review of the English literature. A full term, newborn male who presented immediately after birth with postitional, inspiratory stridor and airway distress. During operative microlaryngoscopy, a well-delineated, non-cystic, stalk-like mass was found in the endolarynx. Biopsy revealed thymic tissue with Hassall's corpuscles, parathyroid tissue and a central core of mature fibroadipose tissue and skeletal muscle. T...
Source: International Journal of Pediatric Otorhinolaryngology Extra - December 13, 2012 Category: ENT & OMF Authors: Jeffrey Cheng, Eileen McKay, Mark D. Rizzi Tags: Case reports Source Type: research

Atypical total necrosis of the long arm of the incus: Two case reports
Conclusion: Placing a gold-wire prosthesis between the malleus and the stapes. At 2 months post-operatively, the ABG was 10db in two cases. (Source: International Journal of Pediatric Otorhinolaryngology Extra)
Source: International Journal of Pediatric Otorhinolaryngology Extra - November 30, 2012 Category: ENT & OMF Authors: Hale Aslan, Sinan Başoğlu, Sedat Öztürkcan, Hüseyin Katılmış Tags: Case reports Source Type: research

Conservative management of dentigerous cyst in a child
This article reports the case of a 10-year-old child who presented permanence of deciduous teeth 51, 52, and 53. Panoramic radiograph showed extensive cystic lesion involving the teeth 11, 12 and 13, which were included. Diagnosis of dentigerous cysts was confirmed by incisional biopsy and the treatment was chosen in order to preserve the associated permanent teeth. At 2 years of follow-up, the impacted teeth are positioning itself spontaneously toward its eruption and the patient was referred for orthodontic assessment. (Source: International Journal of Pediatric Otorhinolaryngology Extra)
Source: International Journal of Pediatric Otorhinolaryngology Extra - November 28, 2012 Category: ENT & OMF Authors: Emeline das Neves de Araújo Lima, Conceição Aparecida Dornelas Monteiro Maia, Alberto Costa Gurgel, Patrícia Teixeira de Oliveira, Ana Miryam Costa de Medeiros Tags: Case reports Source Type: research