Pulmonary Capillary Hemangiomatosis Associated with Connective Tissue Disease: A Report of Four Cases and Review of the Literature

Pulmonary capillary hemangiomatosis (PCH) is a rare vascular proliferation of the septal capillaries. Although it was first described in 1978 [1], there have been fewer than 50 cases reported in the literature [2]. PCH has been described in patients ages 2 to 71, most frequently in young adults [2,3]. PCH is an established cause of clinically evident pulmonary hypertension (PHTN) and classically presents with hemoptysis and pleural effusions [3].

Source: Annals of Diagnostic Pathology - March 21, 2015 Category: Pathology Authors: Shelley I. Odronic, Tathagat Narula, Marie Budev, Carol Farver Tags: Original Contribution Source Type: research