Acid ceramidase improves mitochondrial function and oxidative stress in Niemann-Pick type C disease by repressing STARD1 expression and mitochondrial cholesterol accumulation

Publication date: Available online 19 June 2021Source: Redox BiologyAuthor(s): Sandra Torres, Estel Solsona-Vilarrasa, Susana Nuñez, Nuria Matías, Naroa Insausti-Urkia, Fernanda Castro, Mireia Casasempere, Gemma Fabriás, Josefina Casas, Carlos Enrich, José C. Fernández-Checa, Carmen Garcia-Ruiz
Source: Redox Biology - Category: Biology Source Type: research