Ectopic meningothelial hamartoma of the scalp associated with frontonasal dysplasia

Frontonasal dysplasia and ectopic meningothelial hamartoma of the scalp are both rare entities. The purpose of this report is to describe a unique case in which these anomalies are present simultaneously. CT showed a soft tissue mass with funnel shape morphology in the scalp overlying the posterior fontanelle and MRI shows a mildly enhancing T2 heterogeneous nodule without discernible intracranial extension. Ectopic meningothelial hamartomas should be considered in the differential diagnosis for a midline scalp mass, particularly when a lesion demonstrates a funnel shape morphology and enhancement.

Source: International Journal of Pediatric Otorhinolaryngology Extra - August 26, 2014 Category: ENT & OMF Authors: Daniel Thomas Ginat Tags: Case Report Source Type: research