Difficult airway management in a child with fibrodysplasia ossificans progressiva in status asthmaticus

We present a challenging case of an 11-year-old, 28  kg girl with fibrodysplasia ossificans progressiva. She had severe neck rotation and flexion, kyphosis, scoliosis, decreased chest size (TIS) and extremity contractures. She presented with hypoxia due to parainfluenza virus infection. She became progressively worse requiring continuous nebulized albuterol (1 mg·kg−1·h−1), methylprednisolone, intravenous magnesium, terbutaline infusion, and nasal bilevel positive airway pressure (BiPAP). Approaching respiratory failure, anesthesiology and otolaryngology were consulted to evaluate and secure the airway.
Source: Journal of Clinical Anesthesia - Category: Anesthesiology Authors: Tags: Correspondence Source Type: research