Long QT syndrome with a functional 2:1 block and multilevel conduction disease

A 2-year-old female presented acutely following a three-week history of intermittent fever and lethargy. She was paradoxically bradycardic in the context of fever. An electrocardiogram illustrated multilevel conduction disease and a markedly prolonged QT interval with functional 2:1 atrioventricular block and multilevel conduction disease. Routine baseline aetiological investigations confirmed normal renal and thyroid biochemistry and no evidence of an infective cause or systemic inflammatory response.

Source: Progress in Pediatric Cardiology - July 10, 2018 Category: Cardiology Authors: S. Elston, J.P. Kaski, L.D. Starling Source Type: research