Spondylectomy for primary Ewing's lumbar sarcoma in children

Publication date: Available online 30 December 2017Source: Revista Brasileira de Ortopedia (English Edition)Author(s): Carolina Oliveira, Luísa Vital, Francisco Serdoura, André Rodrigues Pinho, Vitorino VeludoAbstractPrimary Ewing's sarcoma in the spine is very rare. The treatment of Ewing's sarcoma is multidisciplinary. There is no consensus on the optimal method of local control; however, en block resection is associated with an improvement in survival rates. The authors report a case of a 5-year-old girl who initially presented low back pain, who was diagnosed with Ewing’ sarcoma according to radiography, magnetic resonance image and bone biopsy. Spondylectomy was performed in accordance with the EuroEwing protocol. At the three-year follow-up, the patient has no restrictions on daily activities, and to date, there has been no evidence of recurrence.ResumoO Sarcoma de Ewing da coluna vertebral é raro. O tratamento é multidisciplinar. Não há consenso sobre o método ideal de controle local do tumor; no entanto, a ressecção em bloco com margens negativas está associada a uma melhoria da sobrevida. Os autores reportam um caso de uma paciente de 5 anos do sexo feminino, que inicialmente se apresentou com dor lombar, tendo sido diagnosticada com sarcoma de Ewing de acordo com o estudo imagiológico por radiografia, ressonância magnética e biópsia óssea. A paciente foi submetida a vertebrectomia após quimioterapia, de acordo com o protocolo EuroEwing. Aos três a...
Source: Revista Brasileira de Ortopedia - Category: Orthopaedics Source Type: research