Transnasal adenoidectomy in mucopolysaccharidosis
Mucopolysaccharide (MPS) diseases are a heterogeneous group of inherited, metabolic disorders characterized by accumulation of partially degraded glycosaminoglycans (GAG) in multiple organ systems. Due to accumulation in the airway, patients often present with multilevel airway obstruction and obstructive sleep apnoea (OSA). Adenotonsillar surgery leads to a significant improvement in the severity of OSA in MPS patients. However, access to secure the airway and for conventional surgery can be challenging, due to limited neck extension, macroglossia and reduced mouth opening.
Source: International Journal of Pediatric Otorhinolaryngology - Category: ENT & OMF Authors: Rebecca Harrison, Simone Schaefer, Laura Warner, Jean Mercer, Simon Jones, Iain Bruce Source Type: research
More News: Adenoidectomy | Adenoids | ENT & OMF | Obstructive Sleep Apnea | Pediatrics | Sleep Disorders | Sleep Medicine | Tonsillectomy and Adenoidectomy