Disharmonious Patterns of Heterotaxy and Isomerism: How Often Are the Classic Patterns Breached? [Congenital Heart Disease]
Conclusions—
Atrial appendage morphology is difficult to assess and not always indicative of bronchopulmonary or abdominal situs. Discordance between bronchopulmonary branching, atrial appendage arrangement, and splenic status was identified in >20% patients with heterotaxy. Independent description of each organ system is required when arrangements are disharmonious among different organ systems.
Source: Circulation: Cardiovascular Imaging - Category: Radiology Authors: Yim, D., Nagata, H., Lam, C. Z., Grosse-Wortmann, L., Seed, M., Jaeggi, E., Yoo, S.-J. Tags: Pediatrics, Congenital Heart Disease, Computerized Tomography (CT), Imaging, Magnetic Resonance Imaging (MRI) Source Type: research
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