Coagulopathy in Zellweger spectrum disorders: a role for vitamin K

ConclusionBleeding complications frequently occur in ZSD patients due to liver disease and vitamin K deficiency. Vitamin K deficiency is partly corrected by vitamin K supplementation orally, and vitamin K administered IV additionally improves vitamin K status, as shown by further decrease of PIVKA-II and improved thrombin generation.
Source: Journal of Inherited Metabolic Disease - Category: Internal Medicine Source Type: research