Primary central nervous system vasculitis and its mimicking diseases – clinical features, outcome, comorbidities and diagnostic results – A case control study

Primary central nervous system vasculitis (PCNSV), also known as isolated angiitis of the CNS, represents a very rare and poorly understood disease that manifests exclusively in the central nervous system (CNS) [1] and that is potentially fatal. Numerous differential diagnoses have to be considered that can mimic either clinical features and/or diagnostic results, which make PCNSV a diagnostic challenge for clinicians [2,3]. According to its rarity and the diagnostic difficulties reliable registry and epidemiologic data still are lacking [4].

Source: Clinical Neurology and Neurosurgery - March 7, 2017 Category: Neurosurgery Authors: J. Becker, P.A. Horn, K. Keyvani, I. Metz, C. Wegner, W. Br ück, F.M. Heinemann, J.C. Schwitalla, P. Berlit, M. Kraemer Source Type: research