Delayed cochlear implantation in post-meningitic deafness and hereditary complement c2 deficiency

We report the case of an adolescent with post-verbal severe/profound sensorineural hearing loss, occurring as a consequence of two bouts of pneumococcal meningitis at 12 and 32 months of age. A possible immunodeficiency was investigated, revealing hereditary complement C2 deficiency (C2D). Given the insufficient benefit from high-power hearing aids, the boy received a cochlear implant (CI) at age 12. Despite the long interval of partial hearing deprivation and the post-meningitic etiology, improvement in open-set speech perception and quality of life were observed.
Source: International Journal of Pediatric Otorhinolaryngology Extra - Category: ENT & OMF Authors: Tags: Case Report Source Type: research