Dyke-Davidoff-Masson Syndrome in a Nigerian

Publication date: Available online 15 September 2016 Source:Epilepsy & Behavior Case Reports Author(s): Philip B. Adebayo, Amnat Bakare, Modupe M. Bello, Opeyemi D. Olaewe, Kolawole W. Wahab Dyke-Davidoff-Masson Syndrome (DDMS) is a rare but an important cause of intractable seizures. DDMS is a diagnostic constellation made up of hemiparesis, seizure, facial asymmetry and intellectual disability with distinct neuro-imaging features. A 27year old lady presented to us with refractory epilepsy, hemiparesis and intellectual disability that compelled her withdrawal from school. Her brain magnetic resonance imaging (MRI) showed cerebral hemiatrophy, calvarial thickening, and hyperpneumatization of the frontal sinuses, in keeping with DDMS. We discussed the diagnostic nuggets and therapeutic implications of DDMS while advocating for early referral and exhaustive evaluation of people with epilepsy in the sub-Saharan African settings.

Source: Epilepsy and Behavior Case Reports - September 15, 2016 Category: Neurology Source Type: research