High Le Fort I osteotomy for correction of mid‐face deformity in Crouzon syndrome Nakajima

Abstract An 18‐year‐old woman with mild Crouzon syndrome was referred with malocclusion and mandibular protrusion. Examination revealed Class III canine and molar relationships, hypoplastic maxilla, 1‐mm overbite, and −2‐mm overjet. Analysis showed 69° sella‐nasion‐A, 73.6° sella‐nasion‐B, and −4.6° A point‐nasion‐B point angles. Polysomnography revealed respiratory disturbance and 6.3% oxygen desaturation indices of 5.4/h and 9.0/h. We performed double‐jaw surgery using high Le Fort I osteotomy and bilateral sagittal split ramus osteotomy for midfacial deformity correction. Twelve months post‐surgery, her measures were 70.8°, 72°, −1.2°, 3.0/h, and 6.1/h, respectively. Esthetics were satisfactory. High Le Fort I osteotomy is effective for midfacial deformity correction in patients with Crouzon syndrome.
Source: Congenital Anomalies - Category: Genetics & Stem Cells Authors: Tags: Case Report Source Type: research